Congenital heart defects are among the leading causes of birth-related deaths, infants morbidity and mortality. The reported case is rare, because prematurely delivered children with such congenital heart defect as Tetralogy of Fallot, are not likely to survive. This is an extremely unique case either and we want to show, that if correct managing of the pregnancy and exact treatment are carried out we observe an excellent outcome; prematurely delivered infant luckily achieved his maturity and is supposed to undergo surgery .